Coenzyme Q10 deficiency

Coenzyme Q10 deficiency
Other namesLeigh syndrome with nephrotic syndrome
Ubiquinone

Coenzyme Q10 deficiency is a deficiency of coenzyme Q10.

It can be associated with COQ2, APTX, PDSS2, PDSS1, CABC1, and COQ9. Some forms may be more treatable than other mitochondrial diseases.